Incidence, predictive factors, and prognosis of chondrosarcoma in patients with Ollier disease and Maffucci syndrome: an international multicenter study of 161 patients

Publisher DOI
PubMed ID
22147000
Description
Enchondromatosis is characterized by the presence of multiple benign cartilage lesions in bone. While Ollier disease is typified by multiple enchondromas, in Maffucci syndrome these are associated with hemangiomas. Studies evaluating the predictive value of clinical symptoms for development of secondary chondrosarcoma and prognosis are lacking. This multi-institute study evaluates the clinical characteristics of patients, to get better insight on behavior and prognosis of these diseases.
Date of Publication
2011
Publication Type
Article
Language(s)
en
Contributor(s)
Verdegaal, Suzan H M
Bovée, Judith V M G
Pansuriya, Twinkal C
Grimer, Robert J
Ozger, Harzem
Jutte, Paul C
San Julian, Mikel
Biau, David J
van der Geest, Ingrid C M
Leithner, Andreas
Streitbürger, Arne
Gouin, Francois G
Campanacci, Domenico A
Marec-Berard, Perrine
Hogendoorn, Pancras C W
Brand, Ronald
Taminiau, Antonie H M
Additional Credits
Series
Oncologist
Publisher
AlphaMed Press
ISSN
1083-7159
Access(Rights)
metadata.only
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